Pulmonary Arterial Hypertension (PAH)


PAH Six-Minute Walk Test

Could a Mobile App Boost the Utility of the Six-Minute Walk Test in PAH?

Pulmonary arterial hypertension (PAH) is a rare, progressive disorder characterized by vascular proliferation and remodeling of the small pulmonary arteries that ultimately causes right heart failure and premature death. The predominant symptom of PAH is dyspnea on exertion, with a decrease in exercise capacity.1 A variety of methods are available for the objective assessment of…
Hagit Baris-Feldman

Israel Emerges as Global Powerhouse in Rare Disease Research

TEL AVIV, Israel — On the 6th floor of Schneider Children’s Hospital in the Tel Aviv suburb of Petah Tikva, 30 children with Alagille syndrome and 2 with lysosomal acid lipase deficiency (LAL-D) receive specialized treatment from a trio of pediatric hepatologists. Across town, at Sheba Medical Center’s Edmond and Lily Safra Children’s Hospital, pediatric…
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Study Suggests sRAGE as a Potential Biomarker for Adult PAH

Researchers found that the plasma concentration of soluble receptor for advanced glycation end products (sRAGE) is a sensitive and accurate biomarker for adult pulmonary arterial hypertension (PAH). They concluded that sRAGE “has comparable diagnostic accuracy to the established heart failure biomarker [N-terminal prohormone of brain natriuretic peptide] and shows even better performance in the distinction…
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NORD Recognizes Progress in Fight Against Rare Disease With 2021 Rare Impact Awards

Under COVID-19’s lingering shadow, the National Organization of Rare Disorders (NORD) has presented its 2021 Rare Impact Awards to 24 pharmaceutical firms, researchers, politicians, and nonprofit groups for their efforts over the past year on behalf of patients with such illnesses. The virtual ceremony was hosted by John Whyte, MD, MPH, chief medical officer at WebMD, with commentary…

PAH Clinical Insights


Caring for PAH Patients Amid the COVID-19 Pandemic

Beyond the headlines and in the cold realities of hospital wards, the COVID-19 pandemic has wreaked havoc as physicians scramble to come up with a list of new protocols to manage the influx of highly contagious patients.  The COVID-19 pandemic has already upended the neatly divided lines in the hospital wards. In the past, separate…

Rare Care Podcast

Noah Greenspan, DPT, founder of New York City’s Pulmonary Wellness & Rehabilitation Center, runs the nonprofit Pulmonary Wellness Foundation. In this interview, he talks about diagnosing and treating pulmonary arterial hypertension.

PAH Meeting Coverage